Laboratory Medicine and Quality Assurance

Table. 11.

Proficiency testing results for organic acid analysis (unit: mmol/mol creatinine)

Year Trial Specimen no. Intended response Reported response No. Reported components No. Median Minimum Maximum
2022 1st CMO-22-01 Ketosis Ketosis 4 3-Hydroxybutyric acid 4 202 134.2 259.3
Acetoacetic acid 4 1,759.5 414.9 10,836.5
CMO-22-02 Oxaluria type I Oxaluria type I 4 Glycolic acid 3 403.1 137.4 850.4
Oxalic acid 4 667.2 248.4 1,388.8
Oxaluria type II Glyoxylic acid 1 151.6
CMO-22-03 No abnormality detected No abnormality detected 4
2nd CMO-22-04 No abnormality detected No abnormality detected 4
CMO-22-05 Propionic acidemia Propionic acidemia 4 3-Hydroxypropionic acid 4 61 38.8 300.9
Methylcitric acid 3 21.1 6.6 55.2
Propionylglycine 4 96.6 67.5 376.5
CMO-22-06 No abnormality detected No abnormality detected 4
2023 1st CMO-23-01 Methylmalonic acidemia Methylmalonic acidemia 4 3-Hydroxypropionic acid 4 300.4 81.1 793.4
Methylcitric acid 4 29.5 10.4 76.6
Methylmalonic acid 4 320.1 169.9 815.2
CMO-23-02 No abnormality detected No abnormality detected 4
CMO-23-03 No abnormality detected No abnormality detected 4
2nd CMO-23-04 No abnormality detected No abnormality 4
CMO-23-05 Glutaric acidemia type I Glutaric acidemia type I 4 3-Hydroxyglutaric acid 3 18.4 10.8 109.2
Glutraric acid 3 12.7 11.8 134.7
Glutaconic acid 3 1.7 1.5 126.6
CMO-23-06 No abnormality detected No abnormality detected 4
Lab Med Qual Assur 2024;46:175~189 https://doi.org/10.15263/jlmqa.2024.46.4.175
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