Proficiency testing results for organic acid analysis (unit: mmol/mol creatinine)
Year | Trial | Specimen no. | Intended response | Reported response | No. | Reported components | No. | Median | Minimum | Maximum |
---|---|---|---|---|---|---|---|---|---|---|
2022 | 1st | CMO-22-01 | Ketosis | Ketosis | 4 | 3-Hydroxybutyric acid | 4 | 202 | 134.2 | 259.3 |
Acetoacetic acid | 4 | 1,759.5 | 414.9 | 10,836.5 | ||||||
CMO-22-02 | Oxaluria type I | Oxaluria type I | 4 | Glycolic acid | 3 | 403.1 | 137.4 | 850.4 | ||
Oxalic acid | 4 | 667.2 | 248.4 | 1,388.8 | ||||||
Oxaluria type II | Glyoxylic acid | 1 | 151.6 | |||||||
CMO-22-03 | No abnormality detected | No abnormality detected | 4 | |||||||
2nd | CMO-22-04 | No abnormality detected | No abnormality detected | 4 | ||||||
CMO-22-05 | Propionic acidemia | Propionic acidemia | 4 | 3-Hydroxypropionic acid | 4 | 61 | 38.8 | 300.9 | ||
Methylcitric acid | 3 | 21.1 | 6.6 | 55.2 | ||||||
Propionylglycine | 4 | 96.6 | 67.5 | 376.5 | ||||||
CMO-22-06 | No abnormality detected | No abnormality detected | 4 | |||||||
2023 | 1st | CMO-23-01 | Methylmalonic acidemia | Methylmalonic acidemia | 4 | 3-Hydroxypropionic acid | 4 | 300.4 | 81.1 | 793.4 |
Methylcitric acid | 4 | 29.5 | 10.4 | 76.6 | ||||||
Methylmalonic acid | 4 | 320.1 | 169.9 | 815.2 | ||||||
CMO-23-02 | No abnormality detected | No abnormality detected | 4 | |||||||
CMO-23-03 | No abnormality detected | No abnormality detected | 4 | |||||||
2nd | CMO-23-04 | No abnormality detected | No abnormality | 4 | ||||||
CMO-23-05 | Glutaric acidemia type I | Glutaric acidemia type I | 4 | 3-Hydroxyglutaric acid | 3 | 18.4 | 10.8 | 109.2 | ||
Glutraric acid | 3 | 12.7 | 11.8 | 134.7 | ||||||
Glutaconic acid | 3 | 1.7 | 1.5 | 126.6 | ||||||
CMO-23-06 | No abnormality detected | No abnormality detected | 4 |